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Rapid Communication | Open Access

Clinical management of a rare melanoma case arising from congenital melanocytic nevus

Ruixin Jianga,d,1Yan Wangb,1Xuhui Mac,1Xinyang XuanyuaneYanjie Zhanga,dBin Jianga()Weizhen Zhangb()Hanlin Zenga,d()
Department of Oncology, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai 201900, China
Department of Oncology, The Third People’s Hospital of Zhengzhou, Zhengzhou, Henan 450000, China
Department of Oral & Maxillofacial- Head and Neck Oncology, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai 200125, China
Shanghai Institute of Precision Medicine, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai 200125, China
Department of Dermatology, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai 200000, China

Peer review under responsibility of Chongqing Medical University.

1 Co-first authors.

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References

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Alikhan A, Ibrahimi OA, Eisen DB. Congenital melanocytic nevi: where are we now? Part Ⅰ. Clinical presentation, epidemiology, pathogenesis, histology, malignant transformation, and neurocutaneous melanosis. J Am Acad Dermatol. 2012;67(4):495.e1–495.e17; quiz 512–4.
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Mir A, Agim NG, Kane AA, Josephs SC, Park JY, Ludwig K. Giant congenital melanocytic nevus treated with trametinib. Pediatrics. 2019;143(3):e20182469.

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Kinsler VA, O’Hare P, Jacques T, Hargrave D, Slater O. MEK inhibition appears to improve symptom control in primary NRAS-driven CNS melanoma in children. Br J Cancer. 2017;116(8):990–993.

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Weyand AC, Mody RJ, Rabah RM, Opipari VP. PD-1 inhibition in congenital pigment synthesizing metastatic melanoma. Pediatr Blood Cancer. 2018;65(1).

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Arance AM, de la Cruz-Merino L, Petrella TM, et al. Lenvatinib (Len) Plus Pembrolizumab (Pembro) for Patients (Pts) with Advanced Melanoma and Confirmed Progression on a PD-1 or PDL1 Inhibitor: Updated Findings of LEAP-004. ASCO Annual Meeting; 2021. Abstract 9504. 2021.
Genes & Diseases
Article number: 101005
Cite this article:
Jiang R, Wang Y, Ma X, et al. Clinical management of a rare melanoma case arising from congenital melanocytic nevus. Genes & Diseases, 2024, 11(3): 101005. https://doi.org/10.1016/j.gendis.2023.05.007
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