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Review Article | Open Access

Chinese expert consensus on diagnosis and management of split cord malformation

Bo Xiu1( ), Fuyun Liu2, Aijia Shang3, Rui Zhang4
Department of Neurosurgery, The 7th Medical Center of PLA General Hospital, Beijing 100700, China
Department of Pediatric Orthopaedics, Zhengzhou University The 3rd Hospital, Zhengzhou 450052, Henan, China
Department of Neurosurgery, The 1st Medical Center of PLA General Hospital, Beijing 100853, China
Department of Neurosurgery, Shandong Provincial Hospital Affiliated to Shandong First Medical University, Ji'nan 250021, Shandong, China
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Abstract

Split cord malformation (SCM) is a neural tube defect that the spinal cord is longitudinally separated into two hemicords with individual functions, which causes severe spinal cord impairment and sensorimotor deficit. As a kind of myelodysplasia and a special type of tethered cord syndrome, SCM is not widely understood, and common issues in the diagnosis and treatment of SCM should be clarified. In this paper, the Chinese Split Cord Malformation Working Group made a consensus for SCM on embryopathogenesis and types, clinical presentations, neuroimaging assessment, indications and principle of the surgery, surgical techniques and nuances, and prognosis and follow up.

Keywords

split cord malformationtethered cord syndromeneural tube defectdiagnosissurgeryconsensus

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Journal of Neurorestoratology
Volume 8 Issue 2,
June 2020
Pages 83-92
DOI: 10.26599/JNR.2020.9040010
Cite this article:
Xiu B, Liu F, Shang A, et al. Chinese expert consensus on diagnosis and management of split cord malformation. Journal of Neurorestoratology, 2020, 8(2): 83-92. https://doi.org/10.26599/JNR.2020.9040010

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Received: 26 April 2020
Revised: 03 June 2020
Accepted: 24 June 2020
Published: 04 August 2020
© The authors 2020

This article is published with open access at http://jnr.tsinghuajournals.com
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